A general dental practitioner should be familiar with certain rare odontogenic entities like fibrodentinosarcoma, which can occur with unerupted or impacted teeth. The knowledge of such rare pathologies usually associated with unerupted/ impacted teeth aids in the early recognition and correct management of these entities, which are often asymptomatic. One such rare, diverse tumor is ameloblastic fibrodentinosarcoma (AFDS), characterized only by sporadic case reports in the literature. It is important to describe the features of this odontogenic entity to general dental practitioners for successful management and to reduce patient morbidity. This report presents a case of AFDS in a 17-year-old woman who reported to our department with a swelling of the right mandible that was associated with an unerupted tooth. The clinical, radiographic, and histologic findings of AFDS are presented, providing the details necessary to assist the primary dental clinical team in management of AFDS.
Keywords: ameloblastic fibrodentinosarcoma, odontogenic tumor, sarcoma